Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839184 | SCV002099125 | uncertain significance | Spinocerebellar ataxia type 29 | 2021-04-09 | criteria provided, single submitter | clinical testing | The inherited heterozygous c.4216A>T (p.Ile1406Phe) missense variant identified in the ITPR1 gene has not been reported in affected individuals in the literature. The variant is absent from the gnomAD database suggesting it is not a common benign variant in the populations represented in that database. The variant affects an evolutionarily conserved residue and is predicted deleterious by multiple in silico tools. Based on the available evidence, the inherited heterozygous c.4216A>T (p.Ile1406Phe) missense variant identified in the ITPR1 gene is reported as a variant of uncertain significance. |