Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Lab, |
RCV004775656 | SCV005382633 | pathogenic | Alstrom syndrome | 2021-08-05 | criteria provided, single submitter | clinical testing | This nonsense variant (c.5722C>T; p.Gln1908*) has not been reported in population databases (gnomAD) and has not been described in the literature. It was found in an unaffected parent of an affected individual. The proband carries this change as well as an ALMS1 framshift variation (c.793dupA, p.Thr265Asnfs*2) in trans. |