Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Blueprint Genetics | RCV001075165 | SCV001240777 | pathogenic | Retinal dystrophy | 2018-10-19 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001217468 | SCV001389310 | pathogenic | Alstrom syndrome | 2023-03-04 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 866836). This premature translational stop signal has been observed in individual(s) with Alström syndrome (PMID: 17594715). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate poor data quality at this position in the gnomAD database. This sequence change creates a premature translational stop signal (p.Arg2512*) in the ALMS1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in ALMS1 are known to be pathogenic (PMID: 17594715). |