Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002462824 | SCV002757071 | likely pathogenic | Brooke-Spiegler syndrome | 2022-11-30 | criteria provided, single submitter | clinical testing | The variant c.2616del (p.(Tyr872*)) in exon 19 of the CYLD gene is not found in the gnomAD database and it changes the protein sequence starting at position 872 and interrupts the reading frame prematurely. This variant was identified in a patient with a clinical diagnosis of Brooke-Spiegler syndrome. ACMG criteria used for classification: PVS1, PM2. |