Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000700474 | SCV000829231 | uncertain significance | Spinocerebellar ataxia type 19/22 | 2018-04-10 | criteria provided, single submitter | clinical testing | This sequence change replaces serine with cysteine at codon 581 of the KCND3 protein (p.Ser581Cys). The serine residue is moderately conserved and there is a moderate physicochemical difference between serine and cysteine. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Tolerated"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals with KCND3-related disease. This variant is not present in population databases (ExAC no frequency). |