Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV004799277 | SCV001431069 | likely pathogenic | Intellectual disability, autosomal dominant 34 | 2020-02-25 | criteria provided, single submitter | clinical testing | The de novo missense variant p.Thr294Ala (also known as p.Thr166Ala) has been reported in the literature as de novo in a female affected with autism spectrum disorder [PMID: 25363768]. The variant is absent from the gnomAD database indicating it is an extremely rare allele in the general population. The p.Thr294Ala affects a highly conserved residue and is predicted deleterious by multiple in silico tools. However, functional studies are required to determine the functional consequences of this variant on normal function of COL4A3BPprotein. |