Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004584201 | SCV005068293 | benign | Christianson syndrome | 2024-04-18 | reviewed by expert panel | curation | The allele frequency of the c.*5_*8delinsTT variant (denoted as c.*5_*6del + c.*8 A>T) in SLC9A6 is 0.27% in European (non-Finnish) sub population in gnomAD v4.0, which is high enough to be classified as benign based on thresholds defined by the ClinGen Rett/Angelman-like Expert Panel for Rett/AS-like conditions (BA1). In summary, the c.*5_*8delinsTT variant in SLC9A6 is classified as benign based on the ACMG/AMP criteria (BA1). |
Eurofins Ntd Llc |
RCV000175063 | SCV000336683 | benign | not specified | 2015-10-16 | criteria provided, single submitter | clinical testing | |
Athena Diagnostics | RCV000993016 | SCV001145710 | uncertain significance | not provided | 2024-04-11 | criteria provided, single submitter | clinical testing | Available data are insufficient to determine the clinical significance of the variant at this time. This variant has not been reported in large, multi-ethnic general populations. (http://gnomad.broadinstitute.org) Computational tools yielded predictions that this variant is unlikely to have an effect on normal RNA splicing. |
Gene |
RCV000993016 | SCV001934938 | likely benign | not provided | 2017-11-06 | criteria provided, single submitter | clinical testing |