Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001316299 | SCV001506908 | uncertain significance | DiGeorge syndrome | 2023-02-14 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with TBX1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change falls in intron 3 of the TBX1 gene. It does not directly change the encoded amino acid sequence of the TBX1 protein. ClinVar contains an entry for this variant (Variation ID: 1017185). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. |
Prevention |
RCV003399092 | SCV004104381 | uncertain significance | TBX1-related disorder | 2023-08-13 | criteria provided, single submitter | clinical testing | The TBX1 c.411-5C>A variant is predicted to interfere with splicing. To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |