Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001588817 | SCV001814292 | pathogenic | not provided | 2019-06-14 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (Lek et al., 2016); Identified in 2 siblings with Knobloch syndrome in published literature (Menzel et al., 2004); This variant is associated with the following publications: (PMID: 14695535) |
OMIM | RCV000018654 | SCV000038937 | pathogenic | Knobloch syndrome | 2004-01-01 | no assertion criteria provided | literature only |