Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003778493 | SCV004628813 | likely benign | not provided | 2023-11-27 | criteria provided, single submitter | clinical testing | |
Department of Biotechnology and Genetic Engineering, |
RCV003447659 | SCV004174822 | uncertain significance | Knobloch syndrome 1 | 2023-11-14 | no assertion criteria provided | research | Based on ACMG criteria, the variant 799-6C>T is predicted as a Variant of Uncertain Significance (VUS). Segregation analysis corroborated a causal link between the VUS within the COL18A1 gene and disease features within a Pakistani family. This variant consistently manifested as a recessive allele in affected family members and was never observed in a homozygous state within the control population database. The rarity of this variant in its monoallelic status in GnomAD and 1000 Genomes (MAF =0.00003) emphasizes its pathogenic potential role of an autosomal recessive disorder. |