Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000422814 | SCV000512854 | uncertain significance | not provided | 2024-02-21 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 31589614) |
Labcorp Genetics |
RCV000422814 | SCV003256243 | pathogenic | not provided | 2023-08-30 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 377800). This variant has not been reported in the literature in individuals affected with DPYS-related conditions. This variant is present in population databases (rs546700169, gnomAD 0.01%). This sequence change creates a premature translational stop signal (p.Arg118*) in the DPYS gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DPYS are known to be pathogenic (PMID: 20362666). |