Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001591758 | SCV001815821 | uncertain significance | Infantile-onset generalized dyskinesia with orofacial involvement | 2020-10-30 | criteria provided, single submitter | clinical testing | The c.2300C>A; (p.Ser767Tyr) missense variant in exon 23 of 23 of PDE10A has not been reported in affected individuals in the available literature. This variant is absent in gnomADv3 indicating it is not a common benign variant in the populations represented in this database. In silico predictors suggest this variant is Benign (REVEL; score: 0.082) and Damaging (SIFT; score: 0.015). Given the evidence regarding its pathogenicity, the c.2300C>A; (p.Ser767Tyr) variant identified in the PDE10A gene is reported as a Variant of Uncertain Significance. |