Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000074409 | SCV002517529 | likely benign | Corneal dystrophy, Fuchs endothelial, 8 | 2024-10-08 | criteria provided, single submitter | clinical testing | The AGBL1 c.3044G>C (p.Cys1015Ser) variant (rs181958589) has been reported as likely benign by laboratories in ClinVar (Variation ID: 88758). GnomAD 4.1.0 frequency is 0.001952 with 6 homozygotes. This frequencyt and number of homozygotes are not compatible with a variant causing the disease. |
Intergen, |
RCV000074409 | SCV004014852 | likely benign | Corneal dystrophy, Fuchs endothelial, 8 | 2023-07-20 | criteria provided, single submitter | clinical testing | |
Ce |
RCV004584605 | SCV005074578 | likely benign | not provided | 2024-06-01 | criteria provided, single submitter | clinical testing | AGBL1: BP4, BS1 |
OMIM | RCV000074409 | SCV000106021 | pathogenic | Corneal dystrophy, Fuchs endothelial, 8 | 2013-10-03 | no assertion criteria provided | literature only |