Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV004732511 | SCV005329649 | uncertain significance | Abetalipoproteinaemia | criteria provided, single submitter | clinical testing | This variant is not observed in the gnomAD population database. In silico analysis tool (SpliceAI) is predicting this variant to result in aberrant splicing of the MTTP gene. Biallelic variants in MTTP are associate with abetalipoproteinemia (MIM# 200100). |