Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000524078 | SCV000620160 | pathogenic | not provided | 2017-08-21 | criteria provided, single submitter | clinical testing | The R353X variant in the CIC gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. The R353X variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). We interpret R353X as a pathogenic variant. |
OMIM | RCV000496553 | SCV000586809 | pathogenic | Intellectual disability, autosomal dominant 45 | 2022-04-21 | no assertion criteria provided | literature only |