Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV005377657 | SCV006032538 | uncertain significance | not specified | 2025-02-20 | criteria provided, single submitter | clinical testing | The c.1354G>A (p.V452M) alteration is located in exon 8 (coding exon 7) of the MIDN gene. This alteration results from a G to A substitution at nucleotide position 1354, causing the valine (V) at amino acid position 452 to be replaced by a methionine (M). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Genetics and Genomics Program, |
RCV004733988 | SCV005367913 | uncertain significance | Congenital long QT syndrome | no assertion criteria provided | research | The c.1354G>A missense variant in MIDN is present in gnomAD with an allele count of 6 and no homozygous individuals reported (PM2). It is present in our patient and his affected brother. SIFT predictions indicate an uncertain impact (0.008). ACMG codes: PM1, PM2. |