Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004385157 | SCV004864314 | pathogenic | Inborn genetic diseases | 2024-01-03 | criteria provided, single submitter | clinical testing | The c.2874dupT (p.S959*) alteration, located in exon 15 (coding exon 15) of the EP300 gene, consists of a duplication of T at position 2874. This changes the amino acid from a serine (S) to a stop codon at amino acid position 959. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. This variant was not reported in population-based cohorts in the Genome Aggregation Database (gnomAD). Based on the available evidence, this alteration is classified as pathogenic. |