Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002012167 | SCV002229617 | likely benign | not provided | 2023-11-14 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003235632 | SCV003934790 | uncertain significance | not specified | 2023-05-11 | criteria provided, single submitter | clinical testing | Variant summary: FLNB c.5051A>G (p.Tyr1684Cys) results in a non-conservative amino acid change in the encoded protein sequence. Five of five in-silico tools predict a damaging effect of the variant on protein function. The variant allele was found at a frequency of 4.4e-05 in 251092 control chromosomes (gnomAD). To our knowledge, no occurrence of c.5051A>G in individuals affected with Larsen Syndrome and no experimental evidence demonstrating its impact on protein function have been reported. One clinical diagnostic laboratory has submitted clinical-significance assessments for this variant to ClinVar after 2014 and classified the variant as likely benign. Based on the evidence outlined above, the variant was classified as uncertain significance. |