Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003318540 | SCV004022593 | pathogenic | not provided | 2023-07-29 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 26491051, 19505475, 15994868, 14991055) |
OMIM | RCV000006770 | SCV000026964 | pathogenic | Atelosteogenesis type I | 2004-04-01 | no assertion criteria provided | literature only |