Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000657866 | SCV000779626 | likely pathogenic | not provided | 2021-10-18 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (Lek et al., 2016); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 30919572, 28571779) |
Genomic Medicine Center of Excellence, |
RCV003989573 | SCV004808068 | uncertain significance | Gamma-glutamylcysteine synthetase deficiency | 2024-03-29 | criteria provided, single submitter | clinical testing |