Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
DASA | RCV001824132 | SCV002073791 | likely pathogenic | Opsismodysplasia | 2022-02-05 | criteria provided, single submitter | clinical testing | The c.24_39del;p.(Gly9Trpfs*13) is a null frameshift variant (NMD) in the INPPL1 gene and predicts alteration of the nonsense-mediate decay - NMD is present in a relevant exon to the transcript - PVS1. This variant is not present in population databases (rs878853119, gnomAD; ABraOM no frequency - http://abraom.ib.usp.br/) - PM2. In summary, the currently available evidence indicates that the variant is likely pathogenic. |