Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000686198 | SCV000813704 | uncertain significance | Immunodeficiency 39 | 2023-06-27 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with glutamine, which is neutral and polar, at codon 15 of the IRF7 protein (p.Arg15Gln). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 566397). This variant has not been reported in the literature in individuals affected with IRF7-related conditions. This variant is present in population databases (rs368180035, gnomAD 0.01%). |
Ambry Genetics | RCV004026228 | SCV004889370 | uncertain significance | not specified | 2024-02-28 | criteria provided, single submitter | clinical testing | The c.44G>A (p.R15Q) alteration is located in exon 1 (coding exon 1) of the IRF7 gene. This alteration results from a G to A substitution at nucleotide position 44, causing the arginine (R) at amino acid position 15 to be replaced by a glutamine (Q). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |