Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004075739 | SCV003541333 | uncertain significance | not specified | 2022-02-24 | criteria provided, single submitter | clinical testing | The c.4633G>A (p.E1545K) alteration is located in exon 29 (coding exon 29) of the ABCA2 gene. This alteration results from a G to A substitution at nucleotide position 4633, causing the glutamic acid (E) at amino acid position 1545 to be replaced by a lysine (K). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV003404144 | SCV004110041 | uncertain significance | ABCA2-related disorder | 2023-01-31 | criteria provided, single submitter | clinical testing | The ABCA2 c.4633G>A variant is predicted to result in the amino acid substitution p.Glu1545Lys. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.0071% of alleles in individuals of African descent in gnomAD (http://gnomad.broadinstitute.org/variant/9-139907920-C-T). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |