Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002244432 | SCV002513071 | uncertain significance | not provided | 2024-02-20 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); Missense variants in this gene are often considered pathogenic (HGMD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Institute of Rare Diseases, |
RCV005052853 | SCV005686798 | likely pathogenic | Autosomal dominant nonsyndromic hearing loss 20 | 2025-01-09 | criteria provided, single submitter | research | PS2;PM2_Supporting;PP3 |