Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000178166 | SCV000230176 | uncertain significance | not provided | 2015-01-27 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001267567 | SCV001445749 | uncertain significance | Inborn genetic diseases | 2016-11-02 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000178166 | SCV001831859 | pathogenic | not provided | 2022-07-31 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); The majority of missense variants in this gene are considered pathogenic (HGMD); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; This variant is associated with the following publications: (PMID: 35054877) |
Mendelics | RCV002247591 | SCV002516211 | likely pathogenic | Autosomal dominant nonsyndromic hearing loss 20 | 2022-05-04 | criteria provided, single submitter | clinical testing |