Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Tartaglia Lab, |
RCV002280595 | SCV002549687 | pathogenic | Pectus excavatum; Microcephaly; Intellectual disability; Atrophy/Degeneration affecting the central nervous system; Hypotonia | criteria provided, single submitter | research | ||
Institute of Human Genetics, |
RCV003224894 | SCV003921011 | likely pathogenic | Autism; Bifid uvula; Global developmental delay; Motor delay; Self-injurious behavior; Delayed speech and language development; Abnormality of the dentition; Long neck; Delayed early-childhood social milestone development; Neurodevelopmental delay; Clinodactyly; Long ear | 2023-03-21 | criteria provided, single submitter | clinical testing | _x000D_ Criteria applied: PS3, PM2_SUP, PM6_SUP, PP3 |
Institute of Human Genetics, |
RCV003985555 | SCV004801693 | pathogenic | See cases | 2023-09-04 | criteria provided, single submitter | clinical testing | ACMG categories: PS1,PS4,PM2,PM6 |
Gene |
RCV004729127 | SCV005332273 | pathogenic | not provided | 2024-03-27 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; In silico analysis suggests this variant may impact gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown.; This variant is associated with the following publications: (PMID: 36369169) |