Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004721933 | SCV005327631 | uncertain significance | not provided | 2024-02-02 | criteria provided, single submitter | clinical testing | Initiation codon variant in a gene for which loss of function is a known mechanism of disease, however, in the absence of functional studies, the actual effect of this sequence change is unknown; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously published as pathogenic or benign to our knowledge |
Fulgent Genetics, |
RCV005023656 | SCV005657222 | uncertain significance | Renal tubular acidosis with progressive nerve deafness | 2023-12-20 | criteria provided, single submitter | clinical testing |