Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004595637 | SCV005088257 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-06-24 | reviewed by expert panel | curation | The variant NM_001754.5(RUNX1):c.1101C>T (p.Gly367=) is a synonymous change. It is not present in any population databases (gnomAD v2.1.1 and v3.1.2) with at least 20x coverage for RUNX1 (PM2_supporting). Furthermore, the variant has a SpliceAI score of ≤ 0.20 (SpliceAI DG:0.11), indicating a low likelihood of affecting splicing. Evolutionary conservation prediction algorithms suggest that the site is not conserved (PhyloP score 1.12 < 2.0) or that the variant is the reference nucleotide in only one primate and/or three mammal species (BP7). Additionally, there is no previous report of this variant. In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: PM2_supporting, BP4, BP7. |
Labcorp Genetics |
RCV001922922 | SCV002183523 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2022-10-13 | criteria provided, single submitter | clinical testing |