Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV002264722 | SCV002546443 | uncertain significance | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2022-04-11 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.1243C>T (p.Gln415Ter) is a null variant predicted to NOT undergo NMD (PVS1_strong SNV tree). In summary, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: PVS1_strong |
Prevention |
RCV000680386 | SCV000807757 | uncertain significance | not provided | 2017-07-17 | criteria provided, single submitter | clinical testing | |
St. |
RCV000761175 | SCV000891091 | uncertain significance | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2021-01-12 | criteria provided, single submitter | clinical testing |