Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004719343 | SCV005326427 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-09-18 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.165G>T (p.Ala55=) is a synonymous variant which has a SpliceAI score ≤ 0.20 (0.02) (BP4). This variant has a SpliceAI score ≤ 0.20 (0.02) and evolutionary conservation algorithms predict the site as not being conserved (PhyloP score ≤ 2.0 (1.33)) (BP7). This variant is completely absent from all population databases with at least 20x coverage for RUNX1 (PM2_supporting). In summary, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BP4, BP7, PM2_supporting. |
Labcorp Genetics |
RCV003514026 | SCV004276837 | benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2023-11-11 | criteria provided, single submitter | clinical testing |