Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV001290694 | SCV001478831 | benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2020-08-08 | reviewed by expert panel | curation | This synonymous variant is present in gnomAD (v2 and v3) at an allele frequency >0.15% with at least >5 alleles in any general continental population (BA1); in addition, the variant was found in homozygosity in the population database (BP2). Although evolutionary conservation prediction algorithms predict the site as being moderately conserved (PhyloP score: 3.03 > 0.1 [-14.1;6.4]) and the variant is not the reference nucleotide in one primate and/or three mammal species, it is predicted by SSF and MES to lead to either an increase in the canonical splice site score or a decrease of the canonical splice site score by no more than 10% and no putative cryptic splice sites are created (BP4). In summary, the clinical significance of this variant is benign. ACMG/AMP criteria applied, as specified by the ClinGen Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BA1, BP2, and BP4. |
Genetic Services Laboratory, |
RCV000194463 | SCV000248755 | benign | not specified | 2018-10-31 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV000194463 | SCV000308032 | benign | not specified | 2016-08-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000471438 | SCV000560767 | benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2024-01-29 | criteria provided, single submitter | clinical testing | |
KCCC/NGS Laboratory, |
RCV003316087 | SCV004015358 | benign | Acute myeloid leukemia | 2023-07-07 | criteria provided, single submitter | clinical testing | |
Breakthrough Genomics, |
RCV004717079 | SCV005310053 | benign | not provided | criteria provided, single submitter | not provided |