Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004595628 | SCV005088250 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-06-24 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.352-141_352-137del variant is an intronic variant which is absent from all population databases, including gnomAD v2.1.1 and v3.1.2, with at least 20x coverage for RUNX1 (PM2_supporting). In addition, splicing algorithms predicted no effect on splicing (SpliceAI score < 0.20) (BP4), and evolutionary conservation prediction algorithms predict the site as not being conserved (PhyloP100way (GRCh38/hg38) scores 0.0926535 to -0.560732 < 2.0 for all deleted nucleotides) (BP7). To our knowledge, this variant has not been found in patients with FPD/AML phenotype, and no functional studies are available. In summary, this variant meets the criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BP4, BP7, PM2_supporting. |
Gene |
RCV001680397 | SCV001898024 | benign | not provided | 2018-06-23 | criteria provided, single submitter | clinical testing |