Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004595620 | SCV005088383 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-06-24 | reviewed by expert panel | curation | MAF of 0.00001617(0.001617%, 11/68046 alleles) in the NFE subpopulation of the gnomAD 3.1.2 cohort is between 0.00015 (0.015%) and 0.0015 (0.15%) (BS1). This variant is detected in a homozygous state in an individual or in a population database 64 times (gnomAD 3.1.2) (BP2). This synonymous/intronic/UTR/frameshift variant has a SpliceAI score ≤ 0.20 (Donor Loss 0.01) (BP4). Evolutionary conservation prediction algorithms predict the site as not being conserved (PhyloP score -0.01 < 2.0 or the variant is the reference nucleotide in one primate and/or three mammal species) (BP7). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BS1, BP2, BP4, BP7 |
Gene |
RCV001595329 | SCV001828672 | benign | not provided | 2019-03-20 | criteria provided, single submitter | clinical testing |