Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV002264732 | SCV002546383 | likely pathogenic | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2022-01-22 | reviewed by expert panel | curation | This variant NM_001754.5(RUNX1):c.502G>T (p.Gly168Ter) is a nonsense variant predicted to undergo NMD (PVS1). This variant is completely absent from all population databases with at least 20x coverage for RUNX1 (PM2_supporting). In summary, this variant meets criteria to be classified as likely pathogenic. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: PVS1 and PM2_supporting. |
NIHR Bioresource Rare Diseases, |
RCV000851806 | SCV000899774 | likely pathogenic | Pancytopenia | 2019-02-01 | criteria provided, single submitter | research | |
Molecular Genetic Pathology Unit, |
RCV003153243 | SCV003840279 | pathogenic | Clonal Cytopenia of Undetermined Significance | no assertion criteria provided | clinical testing |