Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004692073 | SCV005196472 | uncertain significance | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-08-12 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.554A>C (p.Gln185Pro) is a missense variant which is completely absent from all population databases with at least 20x coverage for RUNX1 (PM2_supporting). This variant has a REVEL score >0.75 (0.977) (PP3). This missense variant is located within the Runt Homology Domain (AA 105-204), but does not occur in an established hotspot residue (PM1_supporting). In summary, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: PM2_supporting, PP3, PM1_supporting. |
Prevention |
RCV000680420 | SCV000807791 | uncertain significance | not provided | 2018-04-05 | criteria provided, single submitter | clinical testing |