Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004700669 | SCV005205665 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-08-28 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.59-4T>C is an intronic variant which is not predicted by SpliceAI to impact splicing (BP4). Additionally, an evolutionary conservation algorithm predicts the site as not being highly conserved (PhyloP score = 0.867551 in GRCh38) (BP7). Although the variant is absent from gnomAD v2, v3, and v4 (PM2_Supporting), it has not been reported in cases or the literature. In summary, this variant meets the criteria to be classified as likely benign for hereditary thrombocytopenia and hematologic cancer predisposition syndrome. ACMG/AMP criteria applied, as specified by the ClinGen Myeloid Malignancy VCEP: BP4, BP7, and PM2_Supporting. |
Labcorp Genetics |
RCV002160827 | SCV002470128 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2021-11-12 | criteria provided, single submitter | clinical testing |