Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004699668 | SCV005205718 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-09-10 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.627A>G (p.Lys209=) is a synonymous variant. This variant is completely absent from all population databases with at least 20x coverage for RUNX1 in gnomAD v2.1.1 and v4.0 (PM2_supporting). SpliceAI predicts no impact on splicing (score: 0.00) (BP4). Evolutionary conservation algorithms predict the site as not being conserved (PhyloP score 1.57) (BP7). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: PM2_supporting, BP4, BP7. |
Labcorp Genetics |
RCV002175399 | SCV002345965 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2023-05-02 | criteria provided, single submitter | clinical testing |