Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV003411833 | SCV004123206 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2023-11-13 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.666C>T (p.Ser222=) is a synonymous variant. This variant has been seen 11x in gnomADv2.1 with a MAF of 0.00026 (0.026%, 8/30616 in the South Asian sub-population (BS1). REVEL score not applicable and SpliceAI <=0.20 (BP4). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BS1 and BP4 |
Labcorp Genetics |
RCV000861133 | SCV001001361 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2024-10-25 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV002256560 | SCV002535875 | likely benign | Hereditary cancer-predisposing syndrome | 2021-08-02 | criteria provided, single submitter | curation | |
Ambry Genetics | RCV004958191 | SCV005495331 | likely benign | Inborn genetic diseases | 2024-11-21 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |