Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV002264700 | SCV002546372 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2022-07-07 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.741C>T (p.Pro247=) is a synonymous variant. As such, a REVEL score is not calculable, and there is no predicted effect on protein function. SpliceAI predicted the following: Acceptor loss 0, Donor loss 0, Acceptor gain 0, Donor gain 0. As such, there is no in silico evidence of an effect on splicing(BP4). Evolutionary conservation prediction algorithms predict the site as not being conserved (PhyloP score 1.06724 < 2.0)(BP7). This variant is completely absent from all population databases with at least 20x coverage for RUNX1(PM2_supporting). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BP4, BP7, PM2_supporting. |
Labcorp Genetics |
RCV000456812 | SCV000560768 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2022-02-09 | criteria provided, single submitter | clinical testing |