Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004719404 | SCV005326458 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-09-18 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.747T>A (p.Pro249=) is a synonymous variant which has a SpliceAI score ≤ 0.20 (0.01) (BP4). This variant has a SpliceAI score ≤ 0.20 (0.01) and evolutionary conservation algorithms predict the site as being not conserved (PhyloP score ≤ 2.0 (1.17) (BP7). This variant is completely absent from all population databases with at least 20x coverage for RUNX1 (PM2_Supporting). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BP4, BP7, PM2_supporting. |
Prevention |
RCV003934327 | SCV004753719 | likely benign | RUNX1-related disorder | 2019-10-31 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |