Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004719171 | SCV005326434 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-09-18 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.98-21T>C is an intronic variant. This variant has a MAF of 0.0002794 (0.028%, 19/67998, 19 alleles) in the European (non-Finnish) subpopulation of the gnomAD v3.1.2 cohort, which is between 0.00015 (0.015%) and 0.0015 (0.15%) (BS1). This variant may impact splicing (Splice AI: Acceptor Loss Score = 0.35). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BS1. |
Institute for Clinical Genetics, |
RCV003238683 | SCV002011267 | uncertain significance | not provided | 2021-11-03 | criteria provided, single submitter | clinical testing |