Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004719954 | SCV005326442 | likely benign | Hereditary thrombocytopenia and hematologic cancer predisposition syndrome | 2024-09-18 | reviewed by expert panel | curation | NM_001754.5(RUNX1):c.994G>A (p.Asp332Asn) is a missense variant. This variant has a MAF of 0.0009758 (0.09758%, 5/5124, 5124 alleles) in the East Asian subpopulation of the gnomAD cohort, which is between 0.00015 (0.015%) and 0.0015 (0.15%) (BS1). This missense variant has a REVEL score < 0.50 (0.316) and a SpliceAI score ≤ 0.20 (0.0) (BP4). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Myeloid Malignancy Variant Curation Expert Panel for RUNX1: BS1, BP4. |
Labcorp Genetics |
RCV000694695 | SCV000823152 | likely benign | Hereditary thrombocytopenia and hematological cancer predisposition syndrome associated with RUNX1 | 2024-10-28 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004958016 | SCV005495319 | benign | Inborn genetic diseases | 2024-06-28 | criteria provided, single submitter | clinical testing | This alteration is classified as benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |