Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Bioinformatics Unit, |
RCV001391242 | SCV001593157 | likely pathogenic | Corticosteroid-binding globulin deficiency | 2021-05-11 | no assertion criteria provided | clinical testing | Frameshift deletion, LOF variant, in heterozygous state found in two affected individuals. Variant population frequency is low (less than 0.0002 in ExAC AMR data base). |