Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001819684 | SCV002070778 | uncertain significance | not specified | 2019-05-21 | criteria provided, single submitter | clinical testing | |
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002252708 | SCV002522933 | likely benign | See cases | 2021-12-09 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PM2, BS2, BP4 |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001819684 | SCV005727042 | uncertain significance | not specified | 2024-11-06 | criteria provided, single submitter | clinical testing | Variant summary: CENPE c.4273G>A (p.Gly1425Arg) results in a non-conservative amino acid change in the encoded protein sequence. Four of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 0.00017 in 251292 control chromosomes, predominantly at a frequency of 0.0021 within the African or African-American subpopulation in the gnomAD database. This frequency is not significantly higher than estimated for a pathogenic variant in CENPE causing Microcephaly 13, Primary, Autosomal Recessive, allowing no conclusion about variant significance. To our knowledge, no occurrence of c.4273G>A in individuals affected with Microcephaly 13, Primary, Autosomal Recessive and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 1337198). Based on the evidence outlined above, the variant was classified as uncertain significance. |