Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001945651 | SCV002189104 | likely benign | not provided | 2022-12-02 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV003339826 | SCV004048363 | uncertain significance | Stickler syndrome type 1 | criteria provided, single submitter | clinical testing | The missense variant c.1513C>T (p.Pro505Ser) in COL2A1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency (0.002%) in the gnomad and novel in 1000 genome database. The amino acid Proline at position 505 is changed to a Serine changing protein sequence and it might alter its composition and physico-chemical properties. The variant is predicted to be damaging by PolyPhen2. The residue is conserved across species. For these reasons, this variant has been classified as Uncertain Significance. | |
Division of Genetics, |
RCV003444066 | SCV004171081 | likely pathogenic | Spondyloepiphyseal dysplasia congenita | 2023-11-27 | criteria provided, single submitter | research |