Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
MVZ Medizinische Genetik Mainz | RCV004698929 | SCV005200657 | uncertain significance | Stickler syndrome, type I, nonsyndromic ocular | 2024-07-22 | criteria provided, single submitter | clinical testing | ACMG Criteria: PP3_MOD,PM2_SUP,PP2 |
Ambry Genetics | RCV004981168 | SCV005568875 | uncertain significance | Inborn genetic diseases | 2024-10-06 | criteria provided, single submitter | clinical testing | The c.1553C>G (p.P518R) alteration is located in exon 24 (coding exon 24) of the COL2A1 gene. This alteration results from a C to G substitution at nucleotide position 1553, causing the proline (P) at amino acid position 518 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |