Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001586411 | SCV001812865 | pathogenic | not provided | 2020-12-17 | criteria provided, single submitter | clinical testing | Occurs in the triple helical domain and replaces the glycine in the canonical GlyX-Y repeat; missense substitution of a canonical glycine residue is expected to disrupt normal protein folding and function, and this is an established mechanism of disease (Stenson et al., 2014); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Institute Of Reproduction And Development, |
RCV003155420 | SCV003844099 | likely pathogenic | See cases | 2021-01-18 | no assertion criteria provided | research |