Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV002470031 | SCV002766177 | uncertain significance | not specified | 2022-11-09 | criteria provided, single submitter | clinical testing | Variant summary: COL4A1 c.1605C>A (p.Phe535Leu) results in a non-conservative amino acid change in the encoded protein sequence. Three of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 6e-05 in 251330 control chromosomes. To our knowledge, no occurrence of c.1605C>A in individuals affected with Porencephaly 1 and no experimental evidence demonstrating its impact on protein function have been reported. No clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Labcorp Genetics |
RCV002571444 | SCV003247025 | likely benign | not provided | 2024-10-26 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005002843 | SCV005632437 | uncertain significance | Autosomal dominant familial hematuria-retinal arteriolar tortuosity-contractures syndrome; Brain small vessel disease 1 with or without ocular anomalies; Hemorrhage, intracerebral, susceptibility to; Retinal arterial tortuosity; Microangiopathy and leukoencephalopathy, pontine, autosomal dominant | 2023-12-22 | criteria provided, single submitter | clinical testing |