Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004729966 | SCV005337149 | likely pathogenic | COL4A1-related disorder | 2024-08-15 | no assertion criteria provided | clinical testing | The COL4A1 c.2096-2delA variant is predicted to result in a deletion affecting a canonical splice site. To our knowledge, this variant has not been reported in the literature or in a large population database, indicating this variant is rare. Variants that disrupt the consensus splice acceptor site in COL4A1 are expected to be pathogenic. This variant is interpreted as likely pathogenic. |