Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Human Genetics and Genomic Medicine, |
RCV003319597 | SCV004023396 | likely pathogenic | Brain small vessel disease 1 with or without ocular anomalies | 2023-06-19 | criteria provided, single submitter | clinical testing | The detected change is not reported in the general population (gnomAD) (as of June 19, 2023). It has not yet been described in the ClinVar database or in the literature. Bioinformatically, the change is classified as "likely disease-causing" (PolyPhen2, Mutation Taster, SIFT, CADDphred 28.5). The variant was not detected in the parental samples. The variant is currently to be regarded as a "likely pathogenic variant" (ACMG criteria). |